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12908359
Distrofia de Duchenne
Description
Si lo toman den créditos
Mind Map by
Vanya Rendón
, updated more than 1 year ago
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Created by
Vanya Rendón
over 6 years ago
4
0
0
Resource summary
Distrofia de Duchenne
1. Causas
Herencia recesiva.
Gen anormal Xp-21
Ausencia de distrofina
2. Manifestaciones Clínicas
Signo Gowers
Hipertrofia de gemelos
Debilidad msc prox
Deterior de marcha
Escoliosis
Dificultad cardioresp
3. Clasificación de distrofias
Emery-Dreifuss
Becker
Cinturas
Facioescapulohumeral
Oculofaríngea
Espina bífida
4. Pronóstico
Fallecimiento temprano (30 años)
Necesidad de aparatos para respirar
6. Tratamiento Fisioterapeútico
Hidroterapia
Terapia ocupacional
Electroterapia
Ejercicios pasivos
5. Objetivos de tratamiento
Facilitar Deambulación
Mantener tono muscular
Retrasar/ prevenir escoliosis
Retrasar progresión de contracturas
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