Outflow obstruction in well child

Description

Paediatrics (Cardio) Mind Map on Outflow obstruction in well child, created by v.djabatey on 28/01/2014.
v.djabatey
Mind Map by v.djabatey, updated more than 1 year ago
v.djabatey
Created by v.djabatey about 10 years ago
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Resource summary

Outflow obstruction in well child
  1. aortic stenosis
    1. aortic valve leaflets partly fused together
      1. giving a restrictive exit from left ventricle
        1. may be 1-3 aortic leaflets
        2. may not be an isolated lesion
          1. often assoc w/ (& so must exclude)
            1. mitral valve stenosis
              1. coarctation of aorta
            2. clinical features
              1. asymptomatic murmur
                1. commonest presentation
                2. presentation of severe stenosis
                  1. reduced exercise tolerance
                    1. chest pain on exertion
                      1. syncope
                      2. presentation in neonatal period
                        1. severe heart failure->shock
                          1. presentation of critical aortic stenosis & duct dependent circulation
                        2. physical signs
                          1. small vol, slow rising pulses
                            1. carotid thrill (always)
                              1. ejection systolic murmur maximal @ upper right sternal edge
                                1. delayed & soft aortic S2
                                  1. apical ejection click
                                2. Ix
                                  1. CXR
                                    1. normal
                                      1. prominent left ventricle w/ post stenotic dilatation of asc aorta
                                      2. ECG
                                        1. left ventricular hypertrophy
                                          1. deep S wave in V2 and tall R wave in V6
                                          2. down going T wave
                                            1. suggests left ventricular strain & aortic stenosis
                                        2. congenital type commoner in boys
                                          1. Mx
                                            1. regular assessment
                                              1. clincal
                                                1. echo
                                                2. if symptomatic on exercise or hihg resting Pa gradient (> 64 mmHg) across aortic valve
                                                  1. balloon valvotomy
                                                    1. generally safe in older kids
                                                      1. more difficult & dangerous in neonates
                                                    2. eventual aortic valve replacement
                                                      1. neonates & kids w/ sig aortic stenosis requiring Rx in 1st few years of life
                                                      2. early Rx
                                                        1. palliative
                                                          1. directed @ delaying valve replacement
                                                          2. avoid competitive sports if severe aortic stenosis
                                                          3. if severe, risk of sudden death
                                                          4. pulmonary stenosis
                                                            1. pulmonary leaflets partly fused together
                                                              1. -> restrictive exit from right ventricle
                                                              2. seen in Noonan's syn
                                                                1. clinical features
                                                                  1. presentation
                                                                    1. asymptomatic
                                                                      1. mild-mod stenosis
                                                                      2. poor exercise tolerance
                                                                        1. severe stenosis
                                                                        2. right ventricular failure/cyanosis
                                                                          1. critical stenosis
                                                                        3. clinical diag
                                                                          1. physical signs
                                                                            1. ejection sys murmur
                                                                              1. best heard at upper left sternal edge
                                                                              2. thrill
                                                                                1. ejection click
                                                                                  1. best heard at upper left sternal edge
                                                                                  2. prominent right ventricular heave
                                                                                    1. when severe stenosis
                                                                                2. Ix
                                                                                  1. CXR
                                                                                    1. normal
                                                                                      1. post stenotic dilatation of pul a
                                                                                      2. ECG
                                                                                        1. right ventricular hypertrophy
                                                                                          1. upright T wave in V1
                                                                                      3. Mx
                                                                                        1. most kids are asymptomatic
                                                                                          1. when Pa grad across pul valve gets sig increased ( > 64 mmHg)
                                                                                            1. intervention needed
                                                                                              1. trans-catheter balloon dilatation
                                                                                        2. adult-type coarctation of aorta
                                                                                          1. uncommon
                                                                                            1. not duct dependent
                                                                                              1. gradually gets more severe over many years
                                                                                                1. usually occurs distal to origin of left subclavian a @ level of ductus arteriosus
                                                                                                  1. commoner in boys than girls
                                                                                                    1. but more common in Turner's syn
                                                                                                    2. clinical features
                                                                                                      1. asymptomatic
                                                                                                        1. systemic hypertension in right arm
                                                                                                          1. ejection systolic murmur
                                                                                                            1. upper sternal edge
                                                                                                              1. or btw shoulder blades
                                                                                                            2. collaterals heard w/ continuous murmur at the back
                                                                                                              1. radio-femoral delay
                                                                                                                1. due to blood bypassing obstruction via collateral vessels in chest wall
                                                                                                                  1. so pulse in legs delayed
                                                                                                                2. weak/absent femoral pulses
                                                                                                                3. Ix
                                                                                                                  1. CXR
                                                                                                                    1. rib notching
                                                                                                                      1. due to development of large collateral intercostal aa running under ribs posteriorly to bypass obstruction
                                                                                                                      2. 3 sign
                                                                                                                        1. w/ visible notch in desc aorta @ site of coarctation
                                                                                                                      3. ECG
                                                                                                                        1. left ventricular hypertrophy
                                                                                                                          1. deep S wave in V2, tall R wave in V6 and upright T wave
                                                                                                                          2. downgoing T wave in V6
                                                                                                                            1. suggest left ventricular strain and severe coarctation and/or HTN
                                                                                                                        2. Mx
                                                                                                                          1. when condition severe
                                                                                                                            1. as assessed by echo
                                                                                                                              1. stent insertion using cardiac catheter
                                                                                                                                1. surgical repair
                                                                                                                              2. complications
                                                                                                                                1. premature coronary heart disease
                                                                                                                                  1. congestive cardiac failure
                                                                                                                                    1. hypertensive encephalopathy
                                                                                                                                      1. intracerebral haemorrhage
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