Quiz
Motor Neuron Disease
This quiz has question types that open in the usual player.
Questions in this quiz (20)
1What is the most common form of Motor Neuron Disease?
- AAmyotrophic Lateral Sclerosis (ALS)
- BHereditary Spastic Paraplegia (HSP)
- CPrimary Lateral Sclerosis (PLS)
2Which type of motor neuron disease exhibits both upper and lower motor neuron degeneration?
- AHereditary Spastic Paraplegia (HSP)
- BPrimary Lateral Sclerosis (PLS)
- CAmyotrophic Lateral Sclerosis (ALS)
3Which type fo Motor Neuron Disease is also referred to as Lou Gehrig's Disease?
- AHereditary Spastic Paraplegia (HSP)
- BPrimary Lateral Sclerosis (PLS)
- CAmyotrophic Lateral Sclerosis (ALS)
4Amyotrophic Lateral Sclerosis typically presents at what age?
- AAround 40
- BAround 20
- CAround 60
- DTeenage years
5The average survival for patients diagnosed with ALS is [blank_start]2-4[blank_end] years, with most eventually dying of [blank_start]respiratory[blank_end] failure
- Arespiratory
- Bheart
- Ccerebral
- D2-4
- E10-20
- F15-20
6The most common symptoms of onset in ALS are spinal onset and bulbar onset. Match the type of onset to its symptoms:
[blank_start]Spinal onset (65%)[blank_end] = Presents with progressive weakness in the arms and the legs
[blank_start]Bulbar onset (25%)[blank_end] = Presents with progressive weakness in the muscles of speech, chewing & swallowing.- ABulbar onset (25%)
- BSpinal onset (65%)
7Which of the following describe Babinski sign
- AFirm stroking of the sole of the foot causes plantarflexion of the foot
- BFirm stroking of the sole of the foot causes dorsiflexion of the foot
- CFirm stroking of the sole of the foot causes eversion of the foot
- DFirm stroking of the sole of the foot causes inversion of the foot
8A clonic jaw reflex would suggest which type of ALS onset?
- ABulbar onset
- BSpinal onset
- CRespiratory onset
9The hands can be a prime indicator of ALS. Split hand syndrome seen in ALS describes the preferential wasting of the [blank_start]thenar[blank_end] muscle group.
- Athenar
- Bhypothenar
10Primary Lateral Sclerosis differs from Amyotrophic Lateral Sclerosis in that it does NOT show signs of [blank_start]lower[blank_end] motor neuron degeneration
- Alower
- Bupper
11Which condition has a better prognosis?
- AAmyotrophic Lateral Sclerosis
- BPrimary Lateral Sclerosis
12There is a strong link between ALS and which type of dementia?
- AFrontotemporal Dementia (Pick's Disease)
- BVascular Dementia
- CAlzheimer's Disease
- DDementia with Lewy Bodies
13Babinski Sign suggests that a patient has experienced [blank_start]upper[blank_end] motor neuron degeneration
- Aupper
- Blower
14What are the two most common causes of death in ALS patients?
- ARespiratory failure
- BPneumonia
- CCardiac failure
- DEndocarditis
- ELung cancer
- FChoking from aspiration
15The pathological hallmark of ALS is the presence of [blank_start]inclusion[blank_end] bodies (abnormal aggregations of protein) in the cytoplasm of motor neurons
- Ainclusion
- Bsubtrusian
- Clewy
- Dtau
- Eubiquitin
16How are reflexes affected by ALS?
- APatients have hyperreflexia due to the UMN degeneration
- BPatients have hyporeflexia due to the LMN degeneration
17[blank_start]Kennedy's[blank_end] Disease is an X-linked recessive condition of the motor neurons in the brainstem and spinal cord. Degeneration of these structures leads to weakness and muscle cramps. It is commonly misdiagnosed as ALS.
- AKennedy's
18Kennedy's Disease [blank_start]only affects males[blank_end]
- Aonly affects males
- Bonly affects females
- Caffects males and females equally
19What is the main treatment for the respiratory failure seen in ALS patients?
- AInvasive ventilation
- BNon-invasive ventilation
20Which sodium channel antagonist can be given to patients with ALS, prolonging their life by 2-3 months?
[blank_start]Riluzole[blank_end]- ARiluzole
Information
- Description
- Motor Neuron Diseases lecture given by Esther Sammler in Week 5
- Author
- Matthew Coulson
- Language
- English
- Views
- 788
- Tags
- Rating
- No ratings yet Rate this quiz