null
US
Sign In
Sign Up for Free
Sign Up
We have detected that Javascript is not enabled in your browser. The dynamic nature of our site means that Javascript must be enabled to function properly. Please read our
terms and conditions
for more information.
Next up
Copy and Edit
You need to log in to complete this action!
Register for Free
16889866
POLICITEMIA VERA
Description
Mind Map on POLICITEMIA VERA, created by Oscar Ulises Durán on 19/02/2019.
Mind Map by
Oscar Ulises Durán
, updated more than 1 year ago
More
Less
Created by
Oscar Ulises Durán
about 5 years ago
24
0
0
Resource summary
POLICITEMIA VERA
Asociada a mutaciones puntuales activadoras de JACK2
Incremento de la producción de eritrocitos, granulocitos y plaquetas
Patogenia
Señalización constitutiva JACK
Células progenitoras transformadas disminuyen los requerimientos de EPO
[EPO] son bajas
Formas secundarias de policitemia: >[EPO]
>Hto; >Viscosidad y aglutinación de la sangre
Trombocitosis y función plaquetaria anormal
Trombosis y hemorragias
97% Mutación del gen JACK2
Sustitución de fenilalanina por valina
Morfología
MO hipercelular
Incremento de progenitores eritrocíticos, granulocíticos y megacariocitos
Clínica
adultos de edad mediana y avanzada
Síntomas asociados a >de eritrocitos, hematocritos y FS
Plétora y cianosis, cefalea, HTA y síntomas GI
Prurito, úlcera péptica, hiperuricemia, gota.
Hemorragias mayores y episodios trombóticos
Leucocitos: 12,000-50,000/mm3; plaquetas>500,000
Tratamiento: Flebotomías
Show full summary
Hide full summary
Want to create your own
Mind Maps
for
free
with GoConqr?
Learn more
.
Similar
Policitemia Vera
Montse Luna
Constitutional Law
jesusreyes88
Computer Science
jacobhuntergoddard
GCSE Biology heart notes
Kamila Woloszyn
IT - The Online World
Summir
History - Germany 1918 - 1945
Grace Evans
Biology (B2)
anjumn10
How did the Cold War develop?
E A
A-Level Revision Tips
Alex Declan
Testing for ions
Joshua Rees
Anatomie - sistemul digestiv 1
Eugeniu Nicolenco
Browse Library